{"id":27418,"date":"2012-07-20T01:17:47","date_gmt":"2012-07-20T05:47:47","guid":{"rendered":"http:\/\/piel-l.org\/blog\/?p=27418"},"modified":"2017-03-31T12:54:46","modified_gmt":"2017-03-31T17:24:46","slug":"sindrome-de-hiper-ige","status":"publish","type":"post","link":"https:\/\/piel-l.org\/blog\/27418","title":{"rendered":"S\u00edndrome de Hiper IgE"},"content":{"rendered":"<p><em><strong>Profesor Dr. Juan Guillermo Chalella <\/strong><\/em><br \/><span style=\"font-size: x-small;\"><em><strong>Conferencia dictada en las Jornadas de Actualizacion terapeutica dermatologica y Estetica 28 al 30 de Junio 2012 Caracas<\/strong><\/em><\/span><\/p>\n<p><!--more--><\/p>\n<p><strong>Que es la INMUNOGLOBULINA E?<\/strong><\/p>\n<p><img loading=\"lazy\" decoding=\"async\" class=\"size-full wp-image-27419 alignnone\" title=\"chalela1\" src=\"http:\/\/piel-l.org\/blog\/wp-content\/uploads\/\/2012\/07\/chalela1.jpg\" alt=\"\" width=\"456\" height=\"275\" srcset=\"https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2012\/07\/chalela1.jpg 456w, https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2012\/07\/chalela1-390x235.jpg 390w\" sizes=\"auto, (max-width: 456px) 100vw, 456px\" \/><\/p>\n<p><strong>A que se le llama SINDROME HIPER IgE \u00bf<\/strong><\/p>\n<ul>\n<li>Altos niveles sericos de IgE<\/li>\n<li>Eczema<\/li>\n<li>Infecciones recurrentes<\/li>\n<\/ul>\n<ul>\n<li>Quimiotaxis neutrof\u00edlica anormal<\/li>\n<li>Producci\u00f3n disminuida de IFN gama<\/li>\n<\/ul>\n<p><strong>Historia del S\u00edndrome de Hiper Ig E <\/strong><\/p>\n<p>1966 S\u00edndrome\u00a0 de Job<\/p>\n<p>Davis, Schaller, Wedgwood Dermatitis cr\u00f3nica, abscesos recurrentes<\/p>\n<p>Infecciones de dif\u00edcil manejo por <em>Estafilococo <\/em>o neumon\u00edas a repetici\u00f3n, rechazo de injertos, pr\u00f3tesis, implantes en inseminaci\u00f3n artificial<\/p>\n<p>1972 Sx Buckey Buckey, Wray, Belmaker Eosinofilia sp, IgE elevada.<\/p>\n<p>Sx Job + Sx Buckey : Sx Hiper IgE<\/p>\n<p>Que es el s\u00edndrome de Hiper Ig E?<\/p>\n<p><img loading=\"lazy\" decoding=\"async\" class=\"alignnone size-full wp-image-27420\" title=\"chalela2\" src=\"http:\/\/piel-l.org\/blog\/wp-content\/uploads\/\/2012\/07\/chalela2.jpg\" alt=\"\" width=\"435\" height=\"289\" srcset=\"https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2012\/07\/chalela2.jpg 435w, https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2012\/07\/chalela2-390x259.jpg 390w\" sizes=\"auto, (max-width: 435px) 100vw, 435px\" \/><\/p>\n<p><strong>Carcaeteristicas del S\u00edndrome de Hiper Ig E<\/strong><\/p>\n<ul>\n<li>Patr\u00f3n autos\u00f3mico dominante principalmente<\/li>\n<li>Todas las razas y sexos<\/li>\n<li>Mutaci\u00f3n en se\u00f1al de transducci\u00f3n y activador de transcripci\u00f3n 3 (STAT3), localizada en cromosoma 17, activada (fosforilaci\u00f3n)<\/li>\n<li>Relaci\u00f3n con IL6,IL11, factor inhibitorio de leucemia, cardiotrofina<\/li>\n<li>Numerosas citocinas y factores neurotr\u00f3ficos asociados<\/li>\n<li>Gp130, IL10, IL17, IL21, IL22, IL23<\/li>\n<li>Numerosos mecanismos proinflamatorios<\/li>\n<li>Relaci\u00f3n Th1\/Th2<\/li>\n<li>Regulaci\u00f3n de neutr\u00f3filos y eosin\u00f3filos<\/li>\n<\/ul>\n<p>Paulson M, Freeman A, Holland SM, Current Op in allergy and Clin Immunol, Vol 8, 527-533, 2008<\/p>\n<p><strong>Presentaciones clinicas<\/strong><\/p>\n<p><img loading=\"lazy\" decoding=\"async\" class=\"alignnone size-full wp-image-27421\" title=\"chalela3\" src=\"http:\/\/piel-l.org\/blog\/wp-content\/uploads\/\/2012\/07\/chalela3.jpg\" alt=\"\" width=\"444\" height=\"223\" srcset=\"https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2012\/07\/chalela3.jpg 444w, https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2012\/07\/chalela3-390x195.jpg 390w\" sizes=\"auto, (max-width: 444px) 100vw, 444px\" \/><\/p>\n<p><img loading=\"lazy\" decoding=\"async\" class=\"alignnone size-full wp-image-27422\" title=\"chalela4\" src=\"http:\/\/piel-l.org\/blog\/wp-content\/uploads\/\/2012\/07\/chalela4.jpg\" alt=\"\" width=\"440\" height=\"222\" srcset=\"https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2012\/07\/chalela4.jpg 440w, https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2012\/07\/chalela4-390x196.jpg 390w\" sizes=\"auto, (max-width: 440px) 100vw, 440px\" \/><\/p>\n<p><strong>Complicaciones<\/strong><\/p>\n<p><img loading=\"lazy\" decoding=\"async\" class=\"alignnone size-full wp-image-27423\" title=\"chalela5\" src=\"http:\/\/piel-l.org\/blog\/wp-content\/uploads\/\/2012\/07\/chalela5.jpg\" alt=\"\" width=\"419\" height=\"331\" srcset=\"https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2012\/07\/chalela5.jpg 419w, https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2012\/07\/chalela5-390x308.jpg 390w\" sizes=\"auto, (max-width: 419px) 100vw, 419px\" \/><\/p>\n<p><strong>Examenes de Laboratorio<\/strong><\/p>\n<p><img loading=\"lazy\" decoding=\"async\" class=\"alignnone size-full wp-image-27424\" title=\"chalela6\" src=\"http:\/\/piel-l.org\/blog\/wp-content\/uploads\/\/2012\/07\/chalela6.jpg\" alt=\"\" width=\"365\" height=\"173\" \/><\/p>\n<p><strong>Tratamiento<\/strong><\/p>\n<p><img loading=\"lazy\" decoding=\"async\" class=\"alignnone size-full wp-image-27425\" title=\"chalela7\" src=\"http:\/\/piel-l.org\/blog\/wp-content\/uploads\/\/2012\/07\/chalela7.jpg\" alt=\"\" width=\"432\" height=\"180\" srcset=\"https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2012\/07\/chalela7.jpg 432w, https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2012\/07\/chalela7-390x162.jpg 390w\" sizes=\"auto, (max-width: 432px) 100vw, 432px\" \/><\/p>\n<hr \/>\n<p>&nbsp;<\/p>\n<div id='gallery-1' class='gallery galleryid-27418 gallery-columns-2 gallery-size-thumbnail'><figure class='gallery-item'>\n\t\t\t<div class='gallery-icon landscape'>\n\t\t\t\t<a href='https:\/\/piel-l.org\/blog\/wp-content\/uploads\/\/2012\/07\/chalela1.jpg'><img loading=\"lazy\" decoding=\"async\" width=\"150\" height=\"150\" src=\"https:\/\/piel-l.org\/blog\/wp-content\/uploads\/\/2012\/07\/chalela1-150x150.jpg\" class=\"attachment-thumbnail size-thumbnail\" alt=\"\" srcset=\"https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2012\/07\/chalela1-150x150.jpg 150w, https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2012\/07\/chalela1-25x25.jpg 25w, https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2012\/07\/chalela1-260x260.jpg 260w\" sizes=\"auto, (max-width: 150px) 100vw, 150px\" \/><\/a>\n\t\t\t<\/div><\/figure><figure class='gallery-item'>\n\t\t\t<div class='gallery-icon landscape'>\n\t\t\t\t<a href='https:\/\/piel-l.org\/blog\/wp-content\/uploads\/\/2012\/07\/chalela2.jpg'><img loading=\"lazy\" decoding=\"async\" width=\"150\" height=\"150\" src=\"https:\/\/piel-l.org\/blog\/wp-content\/uploads\/\/2012\/07\/chalela2-150x150.jpg\" class=\"attachment-thumbnail size-thumbnail\" alt=\"\" srcset=\"https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2012\/07\/chalela2-150x150.jpg 150w, https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2012\/07\/chalela2-25x25.jpg 25w, https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2012\/07\/chalela2-290x289.jpg 290w, https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2012\/07\/chalela2-260x260.jpg 260w\" sizes=\"auto, (max-width: 150px) 100vw, 150px\" \/><\/a>\n\t\t\t<\/div><\/figure><figure class='gallery-item'>\n\t\t\t<div class='gallery-icon landscape'>\n\t\t\t\t<a href='https:\/\/piel-l.org\/blog\/wp-content\/uploads\/\/2012\/07\/chalela3.jpg'><img loading=\"lazy\" decoding=\"async\" width=\"150\" height=\"150\" src=\"https:\/\/piel-l.org\/blog\/wp-content\/uploads\/\/2012\/07\/chalela3-150x150.jpg\" class=\"attachment-thumbnail size-thumbnail\" alt=\"\" srcset=\"https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2012\/07\/chalela3-150x150.jpg 150w, https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2012\/07\/chalela3-25x25.jpg 25w\" sizes=\"auto, (max-width: 150px) 100vw, 150px\" \/><\/a>\n\t\t\t<\/div><\/figure><figure class='gallery-item'>\n\t\t\t<div class='gallery-icon landscape'>\n\t\t\t\t<a href='https:\/\/piel-l.org\/blog\/wp-content\/uploads\/\/2012\/07\/chalela4.jpg'><img loading=\"lazy\" decoding=\"async\" width=\"150\" height=\"150\" src=\"https:\/\/piel-l.org\/blog\/wp-content\/uploads\/\/2012\/07\/chalela4-150x150.jpg\" class=\"attachment-thumbnail size-thumbnail\" alt=\"\" srcset=\"https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2012\/07\/chalela4-150x150.jpg 150w, https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2012\/07\/chalela4-25x25.jpg 25w\" sizes=\"auto, (max-width: 150px) 100vw, 150px\" \/><\/a>\n\t\t\t<\/div><\/figure><figure class='gallery-item'>\n\t\t\t<div class='gallery-icon landscape'>\n\t\t\t\t<a href='https:\/\/piel-l.org\/blog\/wp-content\/uploads\/\/2012\/07\/chalela5.jpg'><img loading=\"lazy\" decoding=\"async\" width=\"150\" height=\"150\" src=\"https:\/\/piel-l.org\/blog\/wp-content\/uploads\/\/2012\/07\/chalela5-150x150.jpg\" class=\"attachment-thumbnail size-thumbnail\" alt=\"\" srcset=\"https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2012\/07\/chalela5-150x150.jpg 150w, https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2012\/07\/chalela5-25x25.jpg 25w, https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2012\/07\/chalela5-290x290.jpg 290w, https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2012\/07\/chalela5-260x260.jpg 260w\" sizes=\"auto, (max-width: 150px) 100vw, 150px\" \/><\/a>\n\t\t\t<\/div><\/figure><figure class='gallery-item'>\n\t\t\t<div class='gallery-icon landscape'>\n\t\t\t\t<a href='https:\/\/piel-l.org\/blog\/wp-content\/uploads\/\/2012\/07\/chalela6.jpg'><img loading=\"lazy\" decoding=\"async\" width=\"150\" height=\"150\" src=\"https:\/\/piel-l.org\/blog\/wp-content\/uploads\/\/2012\/07\/chalela6-150x150.jpg\" class=\"attachment-thumbnail size-thumbnail\" alt=\"\" srcset=\"https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2012\/07\/chalela6-150x150.jpg 150w, https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2012\/07\/chalela6-25x25.jpg 25w\" sizes=\"auto, (max-width: 150px) 100vw, 150px\" \/><\/a>\n\t\t\t<\/div><\/figure><figure class='gallery-item'>\n\t\t\t<div class='gallery-icon landscape'>\n\t\t\t\t<a href='https:\/\/piel-l.org\/blog\/wp-content\/uploads\/\/2012\/07\/chalela7.jpg'><img loading=\"lazy\" decoding=\"async\" width=\"150\" height=\"150\" src=\"https:\/\/piel-l.org\/blog\/wp-content\/uploads\/\/2012\/07\/chalela7-150x150.jpg\" class=\"attachment-thumbnail size-thumbnail\" alt=\"\" srcset=\"https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2012\/07\/chalela7-150x150.jpg 150w, https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2012\/07\/chalela7-25x25.jpg 25w\" sizes=\"auto, (max-width: 150px) 100vw, 150px\" \/><\/a>\n\t\t\t<\/div><\/figure><figure class='gallery-item'>\n\t\t\t<div class='gallery-icon landscape'>\n\t\t\t\t<a href='https:\/\/piel-l.org\/blog\/wp-content\/uploads\/\/2012\/07\/Slide12.jpg'><img loading=\"lazy\" decoding=\"async\" width=\"150\" height=\"150\" src=\"https:\/\/piel-l.org\/blog\/wp-content\/uploads\/\/2012\/07\/Slide12-150x150.jpg\" class=\"attachment-thumbnail size-thumbnail\" alt=\"\" srcset=\"https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2012\/07\/Slide12-150x150.jpg 150w, https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2012\/07\/Slide12-25x25.jpg 25w, https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2012\/07\/Slide12-290x290.jpg 290w, https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2012\/07\/Slide12-260x260.jpg 260w\" sizes=\"auto, (max-width: 150px) 100vw, 150px\" \/><\/a>\n\t\t\t<\/div><\/figure><figure class='gallery-item'>\n\t\t\t<div class='gallery-icon landscape'>\n\t\t\t\t<a href='https:\/\/piel-l.org\/blog\/wp-content\/uploads\/\/2012\/07\/Slide22.jpg'><img loading=\"lazy\" decoding=\"async\" width=\"150\" height=\"150\" src=\"https:\/\/piel-l.org\/blog\/wp-content\/uploads\/\/2012\/07\/Slide22-150x150.jpg\" class=\"attachment-thumbnail size-thumbnail\" alt=\"\" srcset=\"https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2012\/07\/Slide22-150x150.jpg 150w, https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2012\/07\/Slide22-25x25.jpg 25w, https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2012\/07\/Slide22-290x290.jpg 290w, https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2012\/07\/Slide22-260x260.jpg 260w\" sizes=\"auto, (max-width: 150px) 100vw, 150px\" \/><\/a>\n\t\t\t<\/div><\/figure><figure class='gallery-item'>\n\t\t\t<div class='gallery-icon landscape'>\n\t\t\t\t<a href='https:\/\/piel-l.org\/blog\/wp-content\/uploads\/\/2012\/07\/Slide32.jpg'><img loading=\"lazy\" decoding=\"async\" width=\"150\" height=\"150\" src=\"https:\/\/piel-l.org\/blog\/wp-content\/uploads\/\/2012\/07\/Slide32-150x150.jpg\" class=\"attachment-thumbnail size-thumbnail\" alt=\"\" srcset=\"https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2012\/07\/Slide32-150x150.jpg 150w, https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2012\/07\/Slide32-25x25.jpg 25w, https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2012\/07\/Slide32-290x290.jpg 290w, https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2012\/07\/Slide32-260x260.jpg 260w\" sizes=\"auto, (max-width: 150px) 100vw, 150px\" \/><\/a>\n\t\t\t<\/div><\/figure><figure class='gallery-item'>\n\t\t\t<div class='gallery-icon landscape'>\n\t\t\t\t<a href='https:\/\/piel-l.org\/blog\/wp-content\/uploads\/\/2012\/07\/Slide42.jpg'><img loading=\"lazy\" decoding=\"async\" width=\"150\" height=\"150\" src=\"https:\/\/piel-l.org\/blog\/wp-content\/uploads\/\/2012\/07\/Slide42-150x150.jpg\" class=\"attachment-thumbnail size-thumbnail\" alt=\"\" srcset=\"https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2012\/07\/Slide42-150x150.jpg 150w, https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2012\/07\/Slide42-25x25.jpg 25w, https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2012\/07\/Slide42-290x290.jpg 290w, https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2012\/07\/Slide42-260x260.jpg 260w\" sizes=\"auto, (max-width: 150px) 100vw, 150px\" \/><\/a>\n\t\t\t<\/div><\/figure>\n\t\t<\/div>\n\n<p>&nbsp;<\/p>\n","protected":false},"excerpt":{"rendered":"<p>Profesor Dr. Juan Guillermo Chalella Conferencia dictada en las Jornadas de Actualizacion terapeutica dermatologica y Estetica 28 al 30 de Junio 2012 Caracas<\/p>\n","protected":false},"author":50,"featured_media":27428,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[11,252],"tags":[],"class_list":["post-27418","post","type-post","status-publish","format-standard","has-post-thumbnail","","category-secciones-de-colaboradores","category-psicodermatosis"],"_links":{"self":[{"href":"https:\/\/piel-l.org\/blog\/wp-json\/wp\/v2\/posts\/27418","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/piel-l.org\/blog\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/piel-l.org\/blog\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/piel-l.org\/blog\/wp-json\/wp\/v2\/users\/50"}],"replies":[{"embeddable":true,"href":"https:\/\/piel-l.org\/blog\/wp-json\/wp\/v2\/comments?post=27418"}],"version-history":[{"count":0,"href":"https:\/\/piel-l.org\/blog\/wp-json\/wp\/v2\/posts\/27418\/revisions"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/piel-l.org\/blog\/wp-json\/wp\/v2\/media\/27428"}],"wp:attachment":[{"href":"https:\/\/piel-l.org\/blog\/wp-json\/wp\/v2\/media?parent=27418"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/piel-l.org\/blog\/wp-json\/wp\/v2\/categories?post=27418"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/piel-l.org\/blog\/wp-json\/wp\/v2\/tags?post=27418"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}