{"id":3191,"date":"2008-07-04T23:38:15","date_gmt":"2008-07-05T03:38:15","guid":{"rendered":"http:\/\/piel-l.org\/blog\/?p=3191"},"modified":"2008-07-05T10:44:48","modified_gmt":"2008-07-05T14:44:48","slug":"eritroqueratodermia","status":"publish","type":"post","link":"https:\/\/piel-l.org\/blog\/3191","title":{"rendered":"Eritroqueratodermia"},"content":{"rendered":"<p align=\"left\"><img loading=\"lazy\" decoding=\"async\" class=\"alignnone size-full wp-image-3226\" src=\"http:\/\/piel-l.org\/blog\/wp-content\/uploads\/2008\/06\/202\/biomedicina_ucv.jpg\" title=\"biomedicina_ucv\" width=\"231\" height=\"96\" \/><br \/> <strong>Postgrado de Dermatolog\u00eda del Instituto de Biomedicina<br \/> Director del Postgrado Dr. Ricardo Perez Alfonso <\/strong><\/p>\n<p><strong>Autores: <\/strong><strong>Rivera Z, Che-Le\u00f3n V, Bravo N, Duran Y, Misticone S, Oliver M, Henriquez J.J, Piquero J, Kannee C. Instituto de Biomedicina Hospital Vargas. Caracas Venezuela<\/strong><\/p>\n<p>Paciente femenina de 9 a\u00f1os de edad producto de Embarazo a t\u00e9rmino, sin antecedentes de hospitalizaciones, ni cirug\u00edas. Inicia su enfermedad a los 9 meses de edad con placas hiperquerat\u00f3sicas polic\u00edclicas, fijas, bien delimitadas en ambas mejilla que van progresando en forma lenta a trav\u00e9s del tiempo, aumentando en numero y tama\u00f1o, localizadas especialmente en articulaciones: codos, rodilla tal\u00f3n.<\/p>\n<p><!--more--> <\/p>\n<p>Luego de acudir a m\u00faltiples centros asistenciales acude a nuestro Instituto en Febrero del&nbsp; 2005 .<\/p>\n<p>Perfil investigaci\u00f3n&nbsp; rutina: Hematologia, Quimica, serologia, Rayos X de torax : DLN&nbsp;<\/p>\n<p>An\u00e1lisis diagn\u00f3stico<\/p>\n<p>&#8211; PACIENTE CON TRASTORNO CUT\u00c1NEO HEREDITARIO<\/p>\n<p>Espec\u00edficamente:<\/p>\n<p>TRASTORNO DE LA  QUERATINIZACI\u00d3N<\/p>\n<p>Diagn\u00f3sticos diferenciales cl\u00ednicos<\/p>\n<p>v&nbsp; TRASTORNO ICTIOSIFORME:<\/p>\n<p>o&nbsp;&nbsp; &nbsp;ERITROQUERATODERMIA:<\/p>\n<ul>\n<li>ERITROQUERATODERMIA VARIABILIS.<\/li>\n<li>ERITROQUERATODERMIA SIM\u00c9TRICA Y PROGRESIVA.<\/li>\n<\/ul>\n<p>v&nbsp; QUERATODERMIAS PALMOPLANTARES<\/p>\n<p>v&nbsp; OTROS TRASTORNOS<\/p>\n<p>Con el estudio de investigaci\u00f3n histol\u00f3gica, se llega a la conclusi\u00f3n que se trata de una <strong>Eritroqueratodermia simetrica y progresiva<\/strong>, por lo que se sigue la siguiente conducta :<\/p>\n<p>Consulta gen\u00e9tica<\/p>\n<p>Educaci\u00f3n a familiares<\/p>\n<p>Tratamientos Retinoides t\u00f3picos y sist\u00e9micos<\/p>\n<p>Spitz J. Disorders of Cornification. Genodermatoses. USA 2&deg; ed. Lippincott Williams and Wilkins. Pp 26-27.<\/p>\n<p>Mc Kusick VA. Mendelian Inheritance in catalogs of human genes and genetic disorders. Baltamore: Jhona Hopkins&nbsp; University Press.1998.<\/p>\n<hr width=\"100%\" size=\"1\" noshade=\"noshade\" \/><font><a href=\"http:\/\/piel-l.org\/blog\/wp-content\/uploads\/2008\/06\/202\/eritroqueratodermia-fotos.pdf\" target=\"_blank\"><br \/> Descargar Fotograf\u00edas<\/a><\/font><\/p>\n<p> <\/p>\n<hr width=\"100%\" size=\"1\" noshade=\"noshade\" \/> <\/p>\n<p><strong>&nbsp;A la disposici\u00f3n de los lectores una revision Bibliografica de Eritroqueratodermia simetrica y progresiva<\/strong><\/p>\n<hr width=\"100%\" size=\"1\" noshade=\"noshade\" \/>\n<p><font><br \/> &nbsp;<a href=\"http:\/\/piel-l.org\/blog\/wp-content\/uploads\/2008\/06\/202\/eritroqueratodermia-revision.pdf\" target=\"_blank\">Descargar Revisi\u00f3n<\/p>\n<p> <\/a><\/font><\/p>\n<hr width=\"100%\" size=\"1\" noshade=\"noshade\" \/><\/p>\n","protected":false},"excerpt":{"rendered":"<p>Postgrado de Dermatolog\u00eda del Instituto de Biomedicina Director del Postgrado Dr. Ricardo Perez Alfonso Autores: Rivera Z, Che-Le\u00f3n V, Bravo N, Duran Y, Misticone S, Oliver M, Henriquez J.J, Piquero J, Kannee C. Instituto de Biomedicina Hospital Vargas. Caracas Venezuela Paciente femenina de 9 a\u00f1os de edad producto de Embarazo a t\u00e9rmino, sin antecedentes de &hellip;<\/p>\n","protected":false},"author":16,"featured_media":0,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[139],"tags":[125,126],"class_list":["post-3191","post","type-post","status-publish","format-standard","","category-el-modulo-de-los-postgrados","tag-eritroqueratodermia","tag-genodermatosis"],"_links":{"self":[{"href":"https:\/\/piel-l.org\/blog\/wp-json\/wp\/v2\/posts\/3191","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/piel-l.org\/blog\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/piel-l.org\/blog\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/piel-l.org\/blog\/wp-json\/wp\/v2\/users\/16"}],"replies":[{"embeddable":true,"href":"https:\/\/piel-l.org\/blog\/wp-json\/wp\/v2\/comments?post=3191"}],"version-history":[{"count":0,"href":"https:\/\/piel-l.org\/blog\/wp-json\/wp\/v2\/posts\/3191\/revisions"}],"wp:attachment":[{"href":"https:\/\/piel-l.org\/blog\/wp-json\/wp\/v2\/media?parent=3191"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/piel-l.org\/blog\/wp-json\/wp\/v2\/categories?post=3191"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/piel-l.org\/blog\/wp-json\/wp\/v2\/tags?post=3191"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}