{"id":6108,"date":"2009-01-30T09:05:47","date_gmt":"2009-01-30T13:05:47","guid":{"rendered":"http:\/\/piel-l.org\/blog\/?p=6108"},"modified":"2009-01-31T13:30:16","modified_gmt":"2009-01-31T17:30:16","slug":"223-consulte-a-un-colega-n5-que-sindrome-es-este","status":"publish","type":"post","link":"https:\/\/piel-l.org\/blog\/6108","title":{"rendered":"223 Consulte a un Colega N\u00ba5: \u00bfQu\u00e9 s\u00edndrome es este?"},"content":{"rendered":"<p><em>Presentado por Carmen Bastidas (m\u00e9dico dermat\u00f3logo), Varilla (m\u00e9dico internista angiologista), Lolimar Velazquez (m\u00e9dico internista), Rolando Hern\u00e1ndez P\u00e9rez (m\u00e9dico dermat\u00f3logo). Hospital General \u201cDr. Luis Razetti\u201d Barinas\/Venezuela<\/em><\/p>\n<p>Paciente masculino de 20 a\u00f1os de edad, procedente de Barinas\/Venezuela, quien inicia enfermedad actual hace aproximadamente 7 a\u00f1os, con la aparici\u00f3n de edema insidioso en miembros inferiores, de evoluci\u00f3n progresiva.<\/p>\n<p><!--more--><\/p>\n<p>Al examen f\u00edsico aparente buen estado general, m\u00faltiples ef\u00e9lides en \u00e1rea facial y t\u00f3rax superior, pabellones auriculares de baja implantaci\u00f3n, escazas pesta\u00f1as y cejas, con p\u00e1pulas foliculares eritematosas en piel de cejas, desviaci\u00f3n de tabique nasal, orificios de las ventanas nasales amplios, pectus excavatum, linfedema importante en miembros inferiores inferiores, a predominio del derecho, con p\u00e1pulas y ves\u00edculas aisladas, en \u00e1rea de muslos, p\u00e1pulas eritematosas y telangiectasias, que van aumentando en n\u00famero hasta la regi\u00f3n inguinoescrotal donde se aprecian de diferentes di\u00e1metros y de superficie verrugosas.<\/p>\n<p>P\u00e1pulas duras nacaradas y\/o blanquecinas en miembros inferiores.<\/p>\n<p>(Favor ver foto cl\u00ednica IMG3482JPG-IMG3484.JPG- IMG3485.JPG-IMG3486.JPG \u2013IMG3487.JPG)<\/p>\n<figure id=\"attachment_6109\" aria-describedby=\"caption-attachment-6109\" style=\"width: 225px\" class=\"wp-caption alignnone\"><a href=\"http:\/\/piel-l.org\/blog\/wp-content\/uploads\/\/2009\/01\/img_3482.jpg\"><img loading=\"lazy\" decoding=\"async\" class=\"size-medium wp-image-6109\" title=\"img_3482\" src=\"http:\/\/piel-l.org\/blog\/wp-content\/uploads\/\/2009\/01\/img_3482-225x300.jpg\" alt=\"img_3482\" width=\"225\" height=\"300\" srcset=\"https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2009\/01\/img_3482-225x300.jpg 225w, https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2009\/01\/img_3482.jpg 450w\" sizes=\"auto, (max-width: 225px) 100vw, 225px\" \/><\/a><figcaption id=\"caption-attachment-6109\" class=\"wp-caption-text\">img_3482<\/figcaption><\/figure>\n<figure id=\"attachment_6111\" aria-describedby=\"caption-attachment-6111\" style=\"width: 284px\" class=\"wp-caption alignnone\"><a href=\"http:\/\/piel-l.org\/blog\/wp-content\/uploads\/\/2009\/01\/img_34841.jpg\"><img loading=\"lazy\" decoding=\"async\" class=\"size-medium wp-image-6111\" title=\"img_34841\" src=\"http:\/\/piel-l.org\/blog\/wp-content\/uploads\/\/2009\/01\/img_34841-284x300.jpg\" alt=\"img_34841\" width=\"284\" height=\"300\" srcset=\"https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2009\/01\/img_34841-284x300.jpg 284w, https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2009\/01\/img_34841.jpg 450w\" sizes=\"auto, (max-width: 284px) 100vw, 284px\" \/><\/a><figcaption id=\"caption-attachment-6111\" class=\"wp-caption-text\">img_3484<\/figcaption><\/figure>\n<figure id=\"attachment_6112\" aria-describedby=\"caption-attachment-6112\" style=\"width: 225px\" class=\"wp-caption alignnone\"><a href=\"http:\/\/piel-l.org\/blog\/wp-content\/uploads\/\/2009\/01\/img_3485.jpg\"><img loading=\"lazy\" decoding=\"async\" class=\"size-medium wp-image-6112\" title=\"img_3485\" src=\"http:\/\/piel-l.org\/blog\/wp-content\/uploads\/\/2009\/01\/img_3485-225x300.jpg\" alt=\"img_3485\" width=\"225\" height=\"300\" srcset=\"https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2009\/01\/img_3485-225x300.jpg 225w, https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2009\/01\/img_3485.jpg 450w\" sizes=\"auto, (max-width: 225px) 100vw, 225px\" \/><\/a><figcaption id=\"caption-attachment-6112\" class=\"wp-caption-text\">img_3485<\/figcaption><\/figure>\n<figure id=\"attachment_6113\" aria-describedby=\"caption-attachment-6113\" style=\"width: 225px\" class=\"wp-caption alignnone\"><a href=\"http:\/\/piel-l.org\/blog\/wp-content\/uploads\/\/2009\/01\/img_3486.jpg\"><img loading=\"lazy\" decoding=\"async\" class=\"size-medium wp-image-6113\" title=\"img_3486\" src=\"http:\/\/piel-l.org\/blog\/wp-content\/uploads\/\/2009\/01\/img_3486-225x300.jpg\" alt=\"img_3486\" width=\"225\" height=\"300\" srcset=\"https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2009\/01\/img_3486-225x300.jpg 225w, https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2009\/01\/img_3486.jpg 450w\" sizes=\"auto, (max-width: 225px) 100vw, 225px\" \/><\/a><figcaption id=\"caption-attachment-6113\" class=\"wp-caption-text\">img_3486<\/figcaption><\/figure>\n<figure id=\"attachment_6114\" aria-describedby=\"caption-attachment-6114\" style=\"width: 300px\" class=\"wp-caption alignnone\"><a href=\"http:\/\/piel-l.org\/blog\/wp-content\/uploads\/\/2009\/01\/img_3487.jpg\"><img loading=\"lazy\" decoding=\"async\" class=\"size-medium wp-image-6114\" title=\"img_3487\" src=\"http:\/\/piel-l.org\/blog\/wp-content\/uploads\/\/2009\/01\/img_3487-300x225.jpg\" alt=\"img_3487\" width=\"300\" height=\"225\" srcset=\"https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2009\/01\/img_3487-300x225.jpg 300w, https:\/\/piel-l.org\/blog\/wp-content\/uploads\/2009\/01\/img_3487.jpg 800w\" sizes=\"auto, (max-width: 300px) 100vw, 300px\" \/><\/a><figcaption id=\"caption-attachment-6114\" class=\"wp-caption-text\">img_3487<\/figcaption><\/figure>\n<p><br class=\"spacer_\" \/><\/p>\n<p>Ex\u00e1menes de laboratorio de rutina discreta disminuci\u00f3n de prote\u00ednas, resto DLN, Eco Dopler sin hallazgos de insuficiencia venosa ni arterial. No se estudio v\u00edas linf\u00e1ticas.<\/p>\n<p>No antecedentes familiares.<\/p>\n<p>Se tomaron dos muestra para estudio histopatol\u00f3gicos (en espera del laudo)<\/p>\n<p>ID: LINFEDEMA PRIMARIO (Linfedema)<br \/>\n Linfedema m\u00e1s angioqueratoma\/xantomas.<\/p>\n<p>Agradecemos a los distinguidos amigos ayudarnos en la definici\u00f3n o clasificaci\u00f3n de \u00e9ste s\u00edndrome.<\/p>\n<p>\u00bfQue otro examen ustedes solicitar\u00edan.?<\/p>\n<p>\u00bfCual es su opini\u00f3n?<\/p>\n","protected":false},"excerpt":{"rendered":"<p>Presentado por Carmen Bastidas (m\u00e9dico dermat\u00f3logo), Varilla (m\u00e9dico internista angiologista), Lolimar Velazquez (m\u00e9dico internista), Rolando Hern\u00e1ndez P\u00e9rez (m\u00e9dico dermat\u00f3logo). Hospital General \u201cDr. Luis Razetti\u201d Barinas\/Venezuela Paciente masculino de 20 a\u00f1os de edad, procedente de Barinas\/Venezuela, quien inicia enfermedad actual hace aproximadamente 7 a\u00f1os, con la aparici\u00f3n de edema insidioso en miembros inferiores, de evoluci\u00f3n progresiva.<\/p>\n","protected":false},"author":16,"featured_media":0,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[25],"tags":[],"class_list":["post-6108","post","type-post","status-publish","format-standard","","category-consulte-a-un-colega"],"_links":{"self":[{"href":"https:\/\/piel-l.org\/blog\/wp-json\/wp\/v2\/posts\/6108","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/piel-l.org\/blog\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/piel-l.org\/blog\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/piel-l.org\/blog\/wp-json\/wp\/v2\/users\/16"}],"replies":[{"embeddable":true,"href":"https:\/\/piel-l.org\/blog\/wp-json\/wp\/v2\/comments?post=6108"}],"version-history":[{"count":0,"href":"https:\/\/piel-l.org\/blog\/wp-json\/wp\/v2\/posts\/6108\/revisions"}],"wp:attachment":[{"href":"https:\/\/piel-l.org\/blog\/wp-json\/wp\/v2\/media?parent=6108"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/piel-l.org\/blog\/wp-json\/wp\/v2\/categories?post=6108"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/piel-l.org\/blog\/wp-json\/wp\/v2\/tags?post=6108"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}